| Product Name | Anti-ALDH6A1 antibody-RBITC |
|---|---|
| Antibody Type | Primary Antibodies |
| Immunogen | Polypeptide |
| Conjugation | RBITC |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Species Reactivity | HumanMouseRat |
| Concentration | 1mg/ml |
| Purification | Antigen peptide affinity chromatography |
| Gene Symbol | ALDH6A1 |
|---|---|
| Gene Synonyms | 1110038I05Rik MMSADHA MMSDH |
| Gene Full Name | aldehyde dehydrogenase 6 family member A1 |
| Gene Summary | This gene encodes a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jun 2013] |
| Alternative Names | aldehyde dehydrogenase family 6 member A1 aldehyde dehydrogenase family 6 subfamily A1 malonate-semialdehyde dehydrogenase malonate-semialdehyde dehydrogenase (acetylating) methylmalonate semialdehyde dehydrogenase methylmalonate-semialdehyde dehydrogenase [acylating] mitochondrial MGC40271 mitochondrial acylating methylmalonate-semialdehyde dehydrogenase MMSDH testicular tissue protein Li 122 |
| Molecular Weight(MW) | 58kDa |
| Cellular Localization | Mitochondrion，Nucleoplasm |
| SwissProt ID | Q02252 |
|---|
| Form | Liquid |
|---|---|
| Storage Instructions | Shipped at 4°C. Store at +4°C short term (1-2 weeks). Store at -20°C long term. Avoid freeze / thaw cycle. |
| Storage Buffer | Purified antibody in PBS with 0.05% PC300,40% Glycerol. |
