| Product Name | Anti-SGSH antibody-PerCP |
|---|---|
| Antibody Type | Primary Antibodies |
| Immunogen | Polypeptide |
| Conjugation | PerCP |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Species Reactivity | HumanMouseRat |
| Concentration | 1mg/ml |
| Purification | Protein A |
| Gene Symbol | SGSH |
|---|---|
| Gene Synonyms | HSS MPS3A SFMD |
| Gene Full Name | N-sulfoglucosamine sulfohydrolase |
| Gene Summary | This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017] |
| Alternative Names | heparan sulfate sulfatase mucopolysaccharidosis type IIIA sulfoglucosamine sulfamidase sulphamidase |
| Molecular Weight(MW) | 56kDa（observed：54kDa) |
| Source | Rabbit |
| Cellular Localization | Lysosome |
| SwissProt ID | P51688 |
|---|
| Form | Liquid |
|---|---|
| Storage Instructions | Shipped at 4°C. Store at +4°C short term (1-2 weeks). Store at -20°C long term. Avoid freeze / thaw cycle. |
| Storage Buffer | Purified antibody in PBS with 0.05% PC300,40% Glycerol. |
