Rabbit polyclonal antibody to ETFDH (electron-transferring-flavoprotein dehydrogenase)Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67-kDa precursor which is targeted to mitochondria and processed in a single step to a 64-kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia. [provided by RefSeq]
Immunogen
Recombinant protein encompassing a sequence within the N-terminus region of human ETFDH. The exact sequence is proprietary.
Key Feature
Clonality
Polyclonal
Isotype
IgG
Host Species
Rabbit
Tested Applications
WB
*Optimal dilutions/concentrations should be determined by the researcher.
:
Predicted Reactivity
Human, Mouse, Rat, Dog, Cat, Chicken, BovineHuman (100%), Mouse (88%), Rat (90%), Dog (95%), Cat (96%), Chicken (82%), Bovine (94%)
Concentration
1mg/ml (Please refer to the vial label for the specific concentration)
Purification
Affinity purified
Target Information
Gene Synonyms
ETFQO antibody MADD antibody ETFDH antibody ETF-ubiquinone oxidoreductase antibody ETF dehydrogenase antibody "electron transfer flavoprotein-ubiquinone oxidoreductase mitochondrial antibody" ETF-QO antibody electron transfer flavoprotein ubiquinon
Target
ETFDH
Molecular Weight(MW)
68 kDa (note)
Cellular Localization
Mitochondrion inner membrane
Positive Control
Target recombinant protein
Application Notes
*Optimal dilutions/concentrations should be determined by the researcher.
:
Additional Information
Form
Liquid
Storage Instructions
Keep as concentrated solution. Aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles.
Storage Buffer
0.1M Tris, 0.1M Glycine, 10% Glycerol (pH7). 0.01% Thimerosal was added as a preservative.