FAH is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia. This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). Publication Note: This RefSeq record includes a subset of the publications that are available for this gene. Please see the Entrez Gene record to access additional publications.1) Liu, J., (er) Hum Brain Mapp (2007) In press.
Immunogen
Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human FAH.
Key Feature
Clonality
Polyclonal
Host Species
Rabbit
Tested Applications
ELISAWB
FAH antibody can be used for detection of FAH by ELISA at 1:62500. FAH antibody can be used for detection of FAH by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.
Antibody used in WB on Human Liver at 0.2-1 ug/ml.
Application
Antibody used in IHC on human liver, mouse KO at 1:400.
Application
Antibody used in IHC on human liver, mouse KO.
Application
Antibody used in IHC on human liver, mouse KO.
Positive Control
1) Cat. No. XBL-10409 - Fetal Liver Tissue Lysate
Application Notes
FAH antibody can be used for detection of FAH by ELISA at 1:62500. FAH antibody can be used for detection of FAH by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.
Additional Information
Form
Liquid
Storage Instructions
For short periods of storage (days) store at 4˚C. For longer periods of storage, store FAH antibody at -20˚C. As with any antibody avoid repeat freeze-thaw cycles.
Storage Buffer
Antibody is lyophilized in PBS buffer with 2% sucrose. Add 50 μL of distilled water. Final antibody concentration is 1 mg/mL.