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SGSH Antibody

Catalog Number:OM291083
OM291083
Discount Price
OM291083-100ul
1~2 Week
100ul
OM291083-50ul
50ul
OM291083-20ul
20ul
1~2 Week
Product Profile
Product Name SGSH Antibody
Antibody Type Primary Antibodies
Product description SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.1) Sleat, D.E., et al. Mol. Cell Proteomics 5(4):686-701(2006)
Immunogen This SGSH antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 420-449 amino acids from the C-terminal region of human SGSH.
Key Feature
Clonality Polyclonal
Isotype Ig
Host Species Rabbit
Tested Applications WB
For WB starting dilution is: 1:4000
Species Reactivity Human
Concentration 1mg/ml
Purification Affinity purified
Target Information
Gene Symbol SGSH
Alternative Names N-sulphoglucosamine sulphohydrolase
Sulfoglucosamine sulfamidase
Sulphamidase
SGSH
HSS
Molecular Weight(MW) 57 kDa
Database Links
Entrez Gene 6448
Protein Accession P51688
Application

Application

Western Blot at 1:4000 dilution + HepG2 whole cell lysate Lysates/proteins at 20 ug per lane.
Application Notes For WB starting dilution is: 1:4000
Additional Information
Form Liquid
Storage Instructions Store at 4˚C for three months and -20˚C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
Storage Buffer Supplied in PBS with 0.09% (W/V) sodium azide.
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