The protein encoded by this gene is located in the mitochondrion, where it is part of the ubiquinol-cytochrome c reductase complex (also known as complex III). This complex constitutes a part of the mitochondrial respiratory chain. Defects in this gene are a cause of mitochondrial complex III deficiency nuclear type 5. [provided by RefSeq, Jul 2015]
Alternative Names
complex III subunit 2 core protein II core protein II precursor cytochrome bc-1 complex core protein II U MC3DN5 ubiquinol-cytochrome C reductase complex core protein 2 mitochondrial precursor (Complex III subunit II) ubiquinol-cytochrome c reductase core protein II ubiquinol-cytochrome-c reductase complex core protein 2