Western blot
0.2-1 ug/mlELISA Titer: 1:312500Positive Control: Rat Heart| Product Name | Rabbit anti-Gns polyclonal antibody - C-terminal region |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | Gns |
| Immunogen | The immunogen for anti-Gns antibody: synthetic peptide corresponding to a region of Rat |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WB |
| WB:1:500~1:2000 Notes:Optimal dilutions/concentrations should be determined by the researcher. |
|
| Species Reactivity | BovineDogGoatHorseHumanMouseRabbitRatZebra Fish |
| Concentration | 1mg/ml |
| Purification | Affinity purified |
| Gene Symbol | Gns |
|---|---|
| Gene Synonyms | Gns |
| Gene Full Name | Glucosamine (N-acetyl)-6-sulfatase |
| Gene Summary | GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |
| Alternative Names | Gns |
| Molecular Weight(MW) | 58kDa |
| Sequence | 519 amino acids |
| Entrez Gene | 299825 |
|---|---|
| SwissProt ID | Q5M918 |
| Protein Accession | NP_001011989 |
Western blot
0.2-1 ug/mlELISA Titer: 1:312500Positive Control: Rat Heart| Application Notes | WB:1:500~1:2000 Notes:Optimal dilutions/concentrations should be determined by the researcher. |
|---|
| Form | Liquid |
|---|---|
| Storage Instructions | Aliquot and store at -20°C. Avoid repeated freeze / thaw cycles |
| Storage Buffer | phosphate buffered saline , pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. |
