Rabbit Polyclonal antibody to PAHPAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [provided by RefSeq, Jul 2008]
Immunogen
Recombinant protein of human PAH
Key Feature
Clonality
Polyclonal
Isotype
IgG
Host Species
Rabbit
Tested Applications
IHC-PWB
WB: 1:500 - 1:2000. IHC: 1:50 - 1:200:
Species Reactivity
HumanMouseRat
Concentration
1mg/ml
Purification
Affinity purified
Target Information
Gene Synonyms
PKU PH PKU1 phenylalanine hydroxylase
Target
PAH
Molecular Weight(MW)
52 kDa (note)
Application
Application
WB analysis of extracts from various cells using PAH antibody.
Application
IHC-P analysis of human esophageal cancer using PAH antibody at a dilution of 1:100.
Application Notes
WB: 1:500 - 1:2000. IHC: 1:50 - 1:200:
Additional Information
Form
Liquid
Storage Instructions
Store at -20°C (regular) or -80°C (long term). Avoid freeze / thaw cycles.