| Product Name | AASS |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | AASS antibody; Alpha-aminoadipic semialdehyde synthase antibody; mitochondrial antibody; LKR/SDH antibody; |
| Product description | This gene encodes a bifunctional enzyme that catalyzes the first two steps in the mammalian lysine degradation pathway. The N-terminal and the C-terminal portions of this enzyme contain lysine-ketoglutarate reductase and saccharopine dehydrogenase activity, respectively, resulting in the conversion of lysine to alpha-aminoadipic semialdehyde. Mutations in this gene are associated with familial hyperlysinemia. |
| Immunogen | The antiserum was produced against synthesized peptide derived from human AASS. AA range:251-300 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WB |
| WB:1:500-1:2000 |
|
| Species Reactivity | Human |
| Concentration | 1mg/ml |
| Alternative Names | AASS antibody Alpha-aminoadipic semialdehyde synthase antibody mitochondrial antibody LKR/SDH antibody |
|---|---|
| Molecular Weight(MW) | 102 kDa |
| SwissProt ID | Q9UDR5 |
|---|
| Positive Control | Liver, |
|---|---|
| Application Notes | WB:1:500-1:2000 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
