| Product Name | CLC-7 |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | CLCN7 antibody; H(+)/Cl(-) exchange transporter 7 antibody; Chloride channel 7 alpha subunit antibody; Chloride channel protein 7 antibody; ClC-7 antibody; |
| Product description | The product of this gene belongs to the CLC chloride channel family of proteins. Chloride channels play important roles in the plasma membrane and in intracellular organelles. This gene encodes chloride channel 7. Defects in this gene are the cause of osteopetrosis autosomal recessive type 4 (OPTB4), also called infantile malignant osteopetrosis type 2 as well as the cause of autosomal dominant osteopetrosis type 2 (OPTA2), also called autosomal dominant Albers-Schonberg disease or marble disease autosoml dominant. Osteopetrosis is a rare genetic disease characterized by abnormally dense bone, due to defective resorption of immature bone. OPTA2 is the most common form of osteopetrosis, occurring in adolescence or adulthood. |
| Immunogen | The antiserum was produced against synthesized peptide derived from human CLCN7. AA range:10-59 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WB |
| WB:1:500-1:2000 |
|
| Species Reactivity | HumanMouseRat |
| Concentration | 1mg/ml |
| Alternative Names | CLCN7 antibody H(+)/Cl(-) exchange transporter 7 antibody Chloride channel 7 alpha subunit antibody Chloride channel protein 7 antibody ClC-7 antibody |
|---|---|
| Molecular Weight(MW) | 90 kDa |
| SwissProt ID | P51798 |
|---|
| Positive Control | Brain,Epithelium,Lens epithelium,Mammary gland,PCR rescued clones,Skin,Test |
|---|---|
| Application Notes | WB:1:500-1:2000 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
