| Product Name | CLN1 |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | PPT1 antibody; PPT antibody; Palmitoyl-protein thioesterase 1 antibody; PPT-1 antibody; Palmitoyl-protein hydrolase 1 antibody; |
| Product description | The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4). Two transcript variants encoding different isoforms have been found for this gene., |
| Immunogen | The antiserum was produced against synthesized peptide derived from human CLN1. AA range:16-65 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | IHC |
| IHC:1:100-1:300 |
|
| Species Reactivity | HumanMouseRat |
| Concentration | 1mg/ml |
| Alternative Names | PPT1 antibody PPT antibody Palmitoyl-protein thioesterase 1 antibody PPT-1 antibody Palmitoyl-protein hydrolase 1 antibody |
|---|---|
| Molecular Weight(MW) | 37 kDa |
| SwissProt ID | P50897 |
|---|
| Positive Control | Brain,Cerebellum,Liver,Prostate,Testis, |
|---|---|
| Application Notes | IHC:1:100-1:300 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
