| Product Name | CLN6 |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | CLN6 antibody; Ceroid-lipofuscinosis neuronal protein 6 antibody; Protein CLN6 antibody; |
| Product description | This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. |
| Immunogen | The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WBIHC |
| WB:1:500-1:2000 IHC:1:100-1:300 |
|
| Species Reactivity | Human |
| Concentration | 1mg/ml |
| Alternative Names | CLN6 antibody Ceroid-lipofuscinosis neuronal protein 6 antibody Protein CLN6 antibody |
|---|---|
| Molecular Weight(MW) | 40 kDa |
| SwissProt ID | Q9NWW5 |
|---|
| Positive Control | Epithelium,Lung,Urinary bladder, |
|---|---|
| Application Notes | WB:1:500-1:2000 IHC:1:100-1:300 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
