| Product Name | PBFE |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | EHHADH antibody; ECHD antibody; Peroxisomal bifunctional enzyme antibody; PBE antibody; PBFE antibody; |
| Product description | catalytic activity:(3S)-3-hydroxyacyl-CoA = trans-2(or 3)-enoyl-CoA + H(2)O. catalytic activity:(3Z)-dodec-3-enoyl-CoA = (2E)-dodec-2-enoyl-CoA. catalytic activity:(S)-3-hydroxyacyl-CoA + NAD(+) = 3-oxoacyl-CoA + NADH. disease:Absent in patients suffering with peroxisomal disorders such as Zellweger syndrome, neonatal adrenoleukodystrophy and infantile Refsum disease. pathway:Lipid metabolism; fatty acid beta-oxidation. In the C-terminal section; belongs to the 3-hydroxyacyl-CoA dehydrogenase family. In the N-terminal section; belongs to the enoyl-CoA hydratase/isomerase family. subunit:Monomer. tissue specificity:Liver and kidney. Lower amounts seen in the brain. |
| Immunogen | The antiserum was produced against synthesized peptide derived from human EHHADH. AA range:476-525 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WBIHC |
| WB:1:500-1:2000 IHC:1:100-1:300 |
|
| Species Reactivity | HumanRat |
| Concentration | 1mg/ml |
| Alternative Names | EHHADH antibody ECHD antibody Peroxisomal bifunctional enzyme antibody PBE antibody PBFE antibody |
|---|---|
| Molecular Weight(MW) | 80 kDa |
| SwissProt ID | Q08426 |
|---|
| Application Notes | WB:1:500-1:2000 IHC:1:100-1:300 |
|---|
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
