| Product Name | Peroxin 19 |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | PEX19 antibody; HK33 antibody; PXF antibody; OK/SW-cl.22 antibody; Peroxisomal biogenesis factor 19 antibody; 33 kDa housekeeping protein antibody; Peroxin-19 antibody; Peroxisomal farnesylated protein antibody; |
| Product description | This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is |
| Immunogen | The antiserum was produced against synthesized peptide derived from human PEX19. AA range:219-268 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WBIHC |
| WB:1:500-1:2000 IHC:1:100-1:300 |
|
| Species Reactivity | Human |
| Concentration | 1mg/ml |
| Alternative Names | PEX19 antibody HK33 antibody PXF antibody OK/SW-cl.22 antibody Peroxisomal biogenesis factor 19 antibody 33 kDa housekeeping protein antibody Peroxin-19 antibody Peroxisomal farnesylated protein antibody |
|---|---|
| Molecular Weight(MW) | 33 kDa |
| SwissProt ID | P40855 |
|---|
| Positive Control | Brain,Colon adenocarcinoma,Leukocyte,Liver,Lung,Ovary,Placenta,Testis, |
|---|---|
| Application Notes | WB:1:500-1:2000 IHC:1:100-1:300 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
