| Product Name | Peroxin 5 |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | PEX5 antibody; PXR1 antibody; Peroxisomal targeting signal 1 receptor antibody; PTS1 receptor antibody; PTS1R antibody; PTS1-BP antibody; Peroxin-5 antibody; Peroxisomal C-terminal targeting signal import receptor antibody; Peroxisome receptor 1 antibody; |
| Product description | The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of neonatal adrenoleukodystrophy (NALD) |
| Immunogen | Synthesized peptide derived from Peroxin 5 . at AA range: 540-620 |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WB |
| WB:1:500-1:2000 |
|
| Species Reactivity | HumanMouse |
| Concentration | 1mg/ml |
| Alternative Names | PEX5 antibody PXR1 antibody Peroxisomal targeting signal 1 receptor antibody PTS1 receptor antibody PTS1R antibody PTS1-BP antibody Peroxin-5 antibody Peroxisomal C-terminal targeting signal import receptor antibody Peroxisome receptor 1 antibody |
|---|---|
| Molecular Weight(MW) | 70 kDa |
| SwissProt ID | P50542 |
|---|
| Positive Control | Eye,Liver,Testis, |
|---|---|
| Application Notes | WB:1:500-1:2000 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
